English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.
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Clinical description MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities. May Pages ee22 Enfermerad The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. Ocular involvement, which affects the eyelids, conjuctiva, retina, sclera and the choroid plexus, as well as the development of diplopia and ophthalmoplegia as secondary side effects of the neurologic involvementhas also been described.
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Management and treatment Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such debos acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
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From Monday to Friday from 9 a. Additional information Further information on this disease Classification s 3 Gene s 0 Clinical signs and symptoms Publications in PubMed Other website s 7. Go to the members area of the website of the AEDV, dgeos Previous article Next article.
Disease definition Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.
In the year has been indexed in the Medlinedatabase, and has become a vehicle for expressing the most current Spanish medicine and modern. It may more rarely manifest as pericarditis or in other organs such as the lungs, presenting debos pleuritis.
Orphanet: Enfermedad de Degos
Summary Epidemiology Less than cases have been described in the literature. The etiopathogenesis of the disease remains unknown. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted.
Check this box if you wish to receive a copy of your message. Only comments written in English can be processed. As all patients may potentially develop the systemic, life-threatening variant, an annual follow-up is mandatory. Health care resources for this disease Expert centres 69 Diagnostic tests 0 Patient organisations degs Orphan drug s 0.
Are you a health professional able to prescribe or dispense drugs? Systemic lesions may affect the gastrointestinal tract and the central nervous system CNS and are potentially lethal.
enfermedad de degos
For all other comments, please send your remarks via contact us. This condition is chronic and lesions persist over years, often throughout life. The histology of early lesions resembles cutaneous lupus erythematosus see this term. If you are a member of the Deos Many patients have been reported to have defects in blood coagulation.
Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.
More developed lesions show prominent changes in the dermoepidermal junction, with atrophy of the epidermis and an area of sclerosis in the papillary dermis. Systemic manifestations are progressive and may lead to serious complications: Show more Show less.
Later a wedge-shaped connective tissue necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs.
In early stages, histology of lesions may reveal a superficial and deep perivascular lymphocytic infiltration with distinct mucin deposition. Subscribe to our Newsletter. Si continua navegando, consideramos que acepta su uso. Pemphigus Vegetans in the Inguinal Folds. Diagnostic methods Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic.
Prognosis Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions. Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions.
Face, scalp, palms of hands and soles of feet degis rarely involved. Read this article in English. Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial cells have been proposed. Continuing navigation will be considered as acceptance of enfernedad use. Print Send to a friend Export reference Mendeley Statistics.
More developed lesions can imitate lichen sclerosus see this term. No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has been tested successfully in one case with intestinal and CNS manifestations. You can change the settings or obtain more information by clicking here. This item has received. The documents contained in this web site are presented for information purposes only. All deos are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style.
Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
A clinical inspection of the skin should be combined with additional examinations including brain nefermedad resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and abdominal ultrasound, in order to assess the long-term prognosis. MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities.